The Rastelli procedure is typically performed between one and two years of age. Since d-TGA, overriding aorta and DORV are cyanotic heart defects, the child is palliated with a Blalock–Thomas–Taussig shunt in the meantime.
Surgical method
Oxygenated blood is directed from the left ventricle to the aorta using a Gore-Tex patch. The VSD is also sealed with the patch. The pulmonary valve is surgically closed.
In the last seven years of the study, there were seven early deaths (7%) and no surgical fatalities. Univariable analysis revealed that a straddling tricuspid valve (P =.04) and longer aortic crossclamping periods (P =.04) were risk factors for early mortality.
There were 17 late deaths and a patient who had undergone heart transplantation after an average follow-up of 8.5 years.
44 patients underwent reoperations for conduit stenosis, 11 for left ventricular outflow tract obstruction and 28 for interventional catheterization to alleviate conduit stenosis.
There were nine patients with late arrhythmias and five patients who experienced sudden deaths.
At 5, 10, 15 and 20 years, avoidance of death or transplantation (Kaplan-Meier) was 82 percent, 80 percent, 68 percent and 52 percent, respectively.
At 5, 10 and 15 years of followup, the rates of death or reintervention (catheterization or surgical therapy) were 53 percent, 24 percent and 21 percent, respectively.[4]
Conclusions
Overall, the Rastelli procedure has a low initial fatality rate.
Conduit blockage, left ventricular outflow tract obstruction and arrhythmia, on the other hand, are linked to significant late morbidity and mortality.[4]
Almost half of the patients who received the Rastelli operation required heart transplantation or died two decades later.